Marfan’s Syndrome

Marfan’s Syndrome

Sinotubular Ectasia – Marfan’s Syndrome

72712 thoracic aorta sinus of Valsalva aortic sinuses sinotubular junction of ascending aorta sinotubular ectasia fx dilated CTscan Courtesy Ashley DAvidoff MD 72709

Marfan’s Syndrome Sinus of Valsalva Aneurysm

07974c01 heart cardiac right atrium aortic valve aortic sinus fx right atrial filling defect dx sinus of Valsalva aneurysm of the right aortic sinusprolapsing into the right atrium (RA defect) dx Marfan’s Syndrome MRI T1 weighted Davidoff MD 07973.800 07974c01 07974.800

 

Marfan’s Syndrome and Emphysema
Chest x-ray of a patient with Marfan Syndrome showing bullous emphysematous changes in the upper lobes (red arrows), dilated tortuous aorta, and lung hyperinflation. These emphysematous changes can predispose the patient to spontaneous pneumothorax.
Images courtesy of of: Crapo JD, Glassroth J, Karlinsky JB, King TE. Baum’s Textbook of Pulmonary Diseases, 7th ed, Lippincott Williams & Wilkins, Philadelphia 2004. Copyright ¬© 2004 Lippincott Williams & Wilkins.